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International Journal of Hematology

Ausgabe 4/2023

Inhalt (15 Artikel)

Original Article

Real-world safety profile of eculizumab in patients with paroxysmal nocturnal hemoglobinuria, atypical hemolytic uremic syndrome, or generalized myasthenia gravis: an integrated analysis of post-marketing surveillance in Japan

Jun-ichi Nishimura, Tatsuya Kawaguchi, Shuichi Ito, Hiroyuki Murai, Akihiko Shimono, Takahisa Matsuda, Yuji Fukamizu, Hirozumi Akiyama, Hideo Hayashi, Takashi Nakano, Shoichi Maruyama

Original Article

A retrospective analysis of clinical features and treatment outcome in 21 patients with immunoglobulin M-related light-chain amyloidosis in Japan: a study from the Amyloidosis Research Committee

Shin-ichi Fuchida, Mizuki Ogura, Tadao Ishida, Hiroyuki Hata, Hiroshi Handa, Nagaaki Katoh, Chiaki Nakaseko, Kazutaka Sunami, Yuta Katayama, Hironobu Nobata, Kazuiku Oshiro, Shinsuke Iida, Yoshiki Sekijima, Hironobu Naiki, Chihiro Shimazaki

Original Article

Substitution of calcineurin inhibitors with corticosteroids after allogeneic hematopoietic cell transplantation

Shimpei Matsumi, Shun-ichi Kimura, Yuhei Nakamura, Masakatsu Kawamura, Junko Takeshita, Shunto Kawamura, Nozomu Yoshino, Yukiko Misaki, Kazuki Yoshimura, Ayumi Gomyo, Yosuke Okada, Yu Akahoshi, Masaharu Tamaki, Machiko Kusuda, Kazuaki Kameda, Hidenori Wada, Aki Tanihara, Miki Sato, Hideki Nakasone, Shinichi Kako, Yoshinobu Kanda

Original Article

Antibody response after third dose of COVID-19 mRNA vaccination in allogeneic hematopoietic stem cell transplant recipients is comparable to that in healthy counterparts

Erina Takagi, Seitaro Terakura, Hidetsugu Fujigaki, Akinao Okamoto, Kotaro Miyao, Masashi Sawa, Takanobu Morishita, Tatsunori Goto, Yukiyasu Ozawa, Tetsuya Nishida, Nobuaki Fukushima, Kazutaka Ozeki, Ryo Hanajiri, Kuniaki Saito, Makoto Murata, Akihiro Tomita, Hitoshi Kiyoi

Case Report

A case of cold agglutinin syndrome associated with chronic lymphocytic leukaemia harbouring mutations in CARD11 and KMT2D

Masahiko Fukatsu, Yoichi Hamazaki, Yuki Sato, Daisuke Koyama, Takayuki Ikezoe

Open Access Case Report

New onset of hypomegakaryocytic thrombocytopenia with the potential for progression to aplastic anemia after BNT162b2 mRNA COVID-19 vaccination

Mirei Kobayashi, Akio Mori, Yoshitaka Oda, Emi Yokoyama, Minoru Kanaya, Koh Izumiyama, Makoto Saito, Shinya Tanaka, Masanobu Morioka, Takeshi Kondo

Case Report

Mutated ZRSR2 and CUL3 accelerate clonal evolution and confer venetoclax resistance via RAS signaling pathway in blastic plasmacytoid dendritic cell neoplasm

Koichiro Fukuchi, Daisuke Koyama, Maki Takada, Hirotaka Mori, Kiyohito Hayashi, Naomi Asano, Yuki Sato, Masahiko Fukatsu, Motoki Takano, Hiroshi Takahashi, Kayo Shirado-Harada, Satoshi Kimura, Toshiyuki Yamamoto, Takayuki Ikezoe

Case Report

Clinical and genetic features of Japanese cases of MDS associated with VEXAS syndrome

Hiroyoshi Kunimoto, Ayaka Miura, Ayaka Maeda, Naomi Tsuchida, Yuri Uchiyama, Yosuke Kunishita, Yuki Nakajima, Kaoru Takase-Minegishi, Ryusuke Yoshimi, Takuya Miyazaki, Maki Hagihara, Etsuko Yamazaki, Yohei Kirino, Naomichi Matsumoto, Hideaki Nakajima

Case Report

Newly diagnosed extranodal NK/T-cell lymphoma, nasal type, at the injected left arm after BNT162b2 mRNA COVID-19 vaccination

Takuto Tachita, Takenori Takahata, Satoru Yamashita, Toru Ebina, Kosuke Kamata, Kazufumi Yamagata, Yoshiko Tamai, Hirotake Sakuraba

Case Report

Transcriptome sequencing identifies novel EVX fusions involved in transcriptional activation of HOX family genes in pediatric immature T-cell acute lymphoblastic leukemia: two cases reports and a literature review

Xiao Zhang, Bowen Cui, Yizhen Li, Zhiheng Li, Jiajia Zheng, Xinran Chu, Peifang Xiao, Jun Lu, Zheng Wang, Jiannong Cen, Yu Liu, Shaoyan Hu

Case Report

Acute monocytic leukemia with KMT2A::LASP1 developed 9 months after diagnosis of acute megakaryoblastic leukemia in a 2-year-old boy

Takashi Fujita, Hiroko Fukushima, Toru Nanmoku, Yuki Arakawa, Takao Deguchi, Ryoko Suzuki, Yuni Yamaki, Sho Hosaka, Hidetoshi Takada

Case Report

Successful treatment of DOCK8 deficiency by allogeneic hematopoietic cell transplantation from alternative donors

Asuka Kono, Manabu Wakamatsu, Yoshihiro Umezawa, Hideki Muramatsu, Hiroki Fujiwara, Dan Tomomasa, Kento Inoue, Keiichiro Hattori, Tetsuo Mitsui, Hidetoshi Takada, Yoshiyuki Minegishi, Yoshiyuki Takahashi, Masahide Yamamoto, Takehiko Mori, Hirokazu Kanegane

Open Access Letter to the Editor

Measurable residual disease in Japanese patients with relapsed or refractory chronic lymphocytic leukemia treated with venetoclax

Koji Izutsu, Kazuhito Yamamoto, Koji Kato, Takayuki Ishikawa, Noriko Fukuhara, Yasuhito Terui, Ilseung Choi, Sumiko Okubo, Natsumi Ogawa, Mizu Sakai, Yasuko Nishimura, Brenda Chyla, Yan Sun, Dai Maruyama

Erhebliches Risiko für Kehlkopfkrebs bei mäßiger Dysplasie

29.05.2024 Larynxkarzinom Nachrichten

Fast ein Viertel der Personen mit mäßig dysplastischen Stimmlippenläsionen entwickelt einen Kehlkopftumor. Solche Personen benötigen daher eine besonders enge ärztliche Überwachung.

15% bedauern gewählte Blasenkrebs-Therapie

29.05.2024 Urothelkarzinom Nachrichten

Ob Patienten und Patientinnen mit neu diagnostiziertem Blasenkrebs ein Jahr später Bedauern über die Therapieentscheidung empfinden, wird einer Studie aus England zufolge von der Radikalität und dem Erfolg des Eingriffs beeinflusst.

Erhöhtes Risiko fürs Herz unter Checkpointhemmer-Therapie

28.05.2024 Nebenwirkungen der Krebstherapie Nachrichten

Kardiotoxische Nebenwirkungen einer Therapie mit Immuncheckpointhemmern mögen selten sein – wenn sie aber auftreten, wird es für Patienten oft lebensgefährlich. Voruntersuchung und Monitoring sind daher obligat.

Costims – das nächste heiße Ding in der Krebstherapie?

28.05.2024 Onkologische Immuntherapie Nachrichten

„Kalte“ Tumoren werden heiß – CD28-kostimulatorische Antikörper sollen dies ermöglichen. Am besten könnten diese in Kombination mit BiTEs und Checkpointhemmern wirken. Erste klinische Studien laufen bereits.

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