Cor triatriatum dexter in a patient with pectus excavatum

Excerpt

Cor triatriatum dexter (CTD) is an extremely rare congenital anomaly in which the right atrium is divided into two chambers by a membrane caused by persistence of the right valve of the sinus venosus [1]. The persistence of the right leaflet of the venous sinus valve causes a wide range of defects including a prominent Eustachian valve, the Chiari network, and CTD [2]. It has an estimated incidence of around 0.025 % of all congenital heart diseases and is frequently associated with right-sided defects caused by abnormal fetal circulation. Among these, the most frequent are stenosis or atresia of the pulmonary valve, tricuspid valve abnormalities, and atrial septal defects [3]. A patent foramen ovale (PFO) has been shown previously in neonatal and adult patients with CTD [4, 5]. However, CTD and PFO together in a patient with pectus excavatum (PE), which is the most common chest wall deformity affecting 1–300/1,000 individuals, has not been reported in the literature [6]. …